Neurofibromatosis type 2 (NF2) is a genetic disorder characterized by the growth of noncancerous tumors called schwannomas, primarily affecting the nerves in the brain and spinal cord. The most common type of tumor associated with NF2 is the bilateral vestibular schwannomas, which can lead to hearing loss, balance issues, and other neurological problems. NF2 is caused by mutations in the NF2 gene, which is responsible for producing a protein that helps regulate cell growth. This condition is inherited in an autosomal dominant pattern, meaning that an affected individual has a 50% chance of passing the mutation to their offspring. Early diagnosis and management are essential for improving quality of life.