Dentinogenesis imperfecta is a genetic disorder that affects the development of teeth, specifically the dentin, which is the hard tissue beneath the enamel. This condition leads to teeth that are discolored, often appearing blue, gray, or yellow, and they may be more prone to wear, breakage, or decay. It is caused by mutations in genes responsible for the formation of dentin. This condition can occur as part of osteogenesis imperfecta, a disorder that affects bone strength, or it can appear independently. Dentinogenesis imperfecta is inherited in an autosomal dominant pattern, meaning only one copy of the mutated gene from a parent can cause the condition in a child. Regular dental care and monitoring are essential for managing the effects of this disorder.