Argininosuccinate lyase is an enzyme that plays a crucial role in the urea cycle, a metabolic pathway that helps remove ammonia from the body. It catalyzes the conversion of argininosuccinate into arginine and fumarate, facilitating the elimination of excess nitrogen. This enzyme is primarily found in the liver and is essential for maintaining nitrogen balance. Deficiencies in argininosuccinate lyase can lead to a rare genetic disorder known as argininosuccinic aciduria, which can cause serious health issues, including neurological problems and developmental delays.