Aldolase B is an enzyme that plays a crucial role in the metabolism of carbohydrates. It is primarily found in the liver and is responsible for breaking down fructose, a simple sugar found in many foods. This enzyme helps convert fructose into usable energy for the body. Deficiency of Aldolase B can lead to a condition known as hereditary fructose intolerance (HFI). Individuals with HFI cannot properly metabolize fructose, which can result in serious health issues if fructose is consumed. Early diagnosis and dietary management are essential for those affected by this condition.