Frataxin is a protein that plays a crucial role in the body's energy production and iron metabolism. It is primarily found in the mitochondria, the energy-producing structures within cells. Frataxin helps to manage iron levels, preventing the accumulation of excess iron, which can be toxic to cells. Mutations in the gene responsible for producing frataxin are linked to a genetic disorder called Friedreich's ataxia. This condition affects the nervous system and the heart, leading to symptoms such as difficulty walking and coordination problems. Understanding frataxin is essential for developing potential treatments for this disorder.