Alpha-galactosidase A is an enzyme that helps break down complex carbohydrates, specifically those containing galactose. It is produced in the body and plays a crucial role in the metabolism of certain lipids and glycoproteins. Deficiency in this enzyme can lead to a genetic disorder known as Fabry disease, which affects various organs and systems. This enzyme is found in many tissues, including the liver and kidneys. It is also available as a medication to help manage symptoms in individuals with Fabry disease. By supplementing the enzyme, patients can improve their quality of life and reduce complications associated with the disorder.