Hexosaminidase B is an enzyme found in the human body that plays a crucial role in breaking down certain complex molecules called glycosphingolipids. It is primarily active in the lysosomes, which are cellular structures responsible for digestion and waste removal. This enzyme helps maintain cellular health by ensuring that these molecules do not accumulate to toxic levels. Deficiency in Hexosaminidase B can lead to various health issues, including a rare genetic disorder known as Sandhoff disease. This condition affects the nervous system and can result in severe neurological symptoms. Understanding the function of this enzyme is important for diagnosing and developing treatments for related disorders.