Cystathionine Beta-Synthase (CBS) is an enzyme that plays a crucial role in the metabolism of sulfur-containing amino acids, particularly in the conversion of homocysteine to cystathionine. This process is essential for the synthesis of cysteine, which is important for protein production and various cellular functions. Deficiencies in CBS can lead to a condition known as cystathionine beta-synthase deficiency, which is associated with elevated levels of homocysteine in the blood. This can result in various health issues, including cardiovascular problems and developmental delays. Understanding CBS is vital for diagnosing and managing related metabolic disorders.