Acid Alpha-Glucosidase is an enzyme found in the lysosomes of cells. It plays a crucial role in breaking down complex carbohydrates, specifically glycogen, into simpler sugars. This process is essential for maintaining energy levels and proper cellular function. Deficiency of Acid Alpha-Glucosidase leads to a rare genetic disorder known as Pompe disease. This condition results in the accumulation of glycogen in tissues, causing muscle weakness and respiratory issues. Early diagnosis and treatment are important for managing symptoms and improving quality of life for affected individuals.